ClC4

1

Lee RM et al. [Identification of a Novel Calcium (Ca^(2+))-Activated Chloride Channel Accessory Gene in Xenopus laevis].
Mol. Biol. (Mosk.), 2016 Jan-Feb , 50 (106-14).

2

Wang Q et al. Local coupling of TRPC6 to ANO1/TMEM16A channels in smooth muscle cells amplifies vasoconstriction in cerebral arteries.
Am. J. Physiol., Cell Physiol., 2016 May 4 , (ajpcell.00092.2016).

3

Zaika O et al. New perspective of ClC-Kb/2 Cl- channel physiology in the distal renal tubule.
Am. J. Physiol. Renal Physiol., 2016 May 15 , 310 (F923-30).

4

Chen Z et al. Free Energies of Ion Binding in the Bacterial CLC-ec1 Chloride Transporter with Implications for the Transport Mechanism and Selectivity.
J Phys Chem B, 2016 Mar 31 , 120 (3129-39).

5

Perrouin Verbe MA et al. Expression of store-operated channel components in prostate cancer: the prognostic paradox.
Hum. Pathol., 2016 Mar , 49 (77-82).

6

Imbrici P et al. Multidisciplinary study of a new ClC-1 mutation causing myotonia congenita: a paradigm to understand and treat ion channelopathies.
FASEB J., 2016 Jun 20 , ().

7

Yu Y et al. Heart-specific overexpression of the human short CLC-3 chloride channel isoform limits myocardial ischemia-induced ERP and QT prolongation.
Int. J. Cardiol., 2016 Jul 1 , 214 (218-24).

8

Zeng B et al. A novel mutation and a known mutation in the CLCN7 gene associated with relatively stable infantile malignant osteopetrosis in a Chinese patient.
Gene, 2016 Jan 15 , 576 (176-81).

9

De Jesús-Pérez JJ et al. Gating the glutamate gate of CLC-2 chloride channel by pore occupancy.
J. Gen. Physiol., 2016 Jan , 147 (25-37).

10

Riisager A et al. Protein kinase C dependent regulation of ClC-1 channels in active human muscle and its effect on fast and slow gating.
J. Physiol. (Lond.), 2016 Feb 9 , ().

11

Ma MM et al. Threonine532 phosphorylation in ClC-3 channels is required for angiotensin II-induced Cl(-) current and migration in cultured vascular smooth muscle cells.
Br. J. Pharmacol., 2016 Feb , 173 (529-44).

12

Garreta E et al. Myocardial commitment from human pluripotent stem cells: Rapid production of human heart grafts.
Biomaterials, 2016 Aug , 98 (64-78).

13

Lam CS et al. The Onset of H + Ketene Products from Vinoxy Radicals Prepared by Photodissociation of Chloroacetaldehyde at 157 nm.
J Phys Chem A, 2016 Apr 28 , 120 (2521-36).

14

Pedersen TH et al. Role of physiological ClC-1 Cl- ion channel regulation for the excitability and function of working skeletal muscle.
J. Gen. Physiol., 2016 Apr , 147 (291-308).

15

Liu LI et al. Fluid shear stress enhances the cell volume decrease of osteoblast cells by increasing the expression of the ClC-3 chloride channel.
Biomed Rep, 2016 Apr , 4 (408-412).

16

Delgado R et al. Single Ca(2+)-activated Cl(-) channel currents recorded from toad olfactory cilia.
BMC Neurosci, 2016 , 17 (17).

17

Herdean A et al. The Arabidopsis Thylakoid Chloride Channel AtCLCe Functions in Chloride Homeostasis and Regulation of Photosynthetic Electron Transport.
Front Plant Sci, 2016 , 7 (115).

18

Yamazaki J Functional Expression of a Ca(2+)-activated Cl(-) Channel Modulator Involved in Ion Transport and Epithelial Cell Differentiation.
Yakugaku Zasshi, 2016 , 136 (485-90).

19

Hu MY et al. Temperature Modulates the Effects of Ocean Acidification on Intestinal Ion Transport in Atlantic Cod, Gadus morhua.
Front Physiol, 2016 , 7 (198).

20

Cutz E Whole Exome Sequencing Reveals CLCNKB Mutations in a Case of Sudden Unexpected Infant Death.
Pediatr. Dev. Pathol., 2015 Jul-Aug , 18 (339-40).

21

Lopez HU et al. Whole-Exome Sequencing Reveals CLCNKB Mutations in a Case of Sudden Unexpected Infant Death.
Pediatr. Dev. Pathol., 2015 Jul-Aug , 18 (324-6).

22

Arcangeli A et al. Novel perspectives in cancer therapy: Targeting ion channels.
Drug Resist. Updat., 2015 Jul-Aug , 21-22 (11-9).

23

Onur S et al. Association between serum level of ubiquinol and NT-proBNP, a marker for chronic heart failure, in healthy elderly subjects.
Biofactors, 2015 Jan-Feb , 41 (35-43).

24

Bulk E et al. Epigenetic dysregulation of KCa 3.1 channels induces poor prognosis in lung cancer.
Int. J. Cancer, 2015 Sep 15 , 137 (1306-17).

25

Miller C In the beginning: a personal reminiscence on the origin and legacy of ClC-0, the 'Torpedo Cl(-) channel'.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4085-90).

26

Fong P Twenty-five years of CLC chloride transport proteins.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4083-4).

27

Accardi A Structure and gating of CLC channels and exchangers.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4129-38).

28

Imbrici P et al. ClC-1 mutations in myotonia congenita patients: insights into molecular gating mechanisms and genotype-phenotype correlation.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4181-99).

29

Zifarelli G A tale of two CLCs: biophysical insights toward understanding ClC-5 and ClC-7 function in endosomes and lysosomes.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4139-50).

30

Capdevila-Nortes X et al. Structural determinants of interaction, trafficking and function in the ClC-2/MLC1 subunit GlialCAM involved in leukodystrophy.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4165-80).

31

Devuyst O et al. Chloride transporters and receptor-mediated endocytosis in the renal proximal tubule.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4151-64).

32

Barrallo-Gimeno A et al. Regulatory-auxiliary subunits of CLC chloride channel-transport proteins.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4111-27).

33

Portaro S et al. Clinical, Molecular, and Functional Characterization of CLCN1 Mutations in Three Families with Recessive Myotonia Congenita.
Neuromolecular Med., 2015 Sep , 17 (285-96).

34

Dogan Onugoren M et al. Limbic encephalitis due to GABAB and AMPA receptor antibodies: a case series.
J. Neurol. Neurosurg. Psychiatr., 2015 Sep , 86 (965-72).

35

Guzman RE et al. Neuronal ClC-3 Splice Variants Differ in Subcellular Localizations, but Mediate Identical Transport Functions.
J. Biol. Chem., 2015 Oct 23 , 290 (25851-62).

36

Dasari R et al. Wittig derivatization of sesquiterpenoid polygodial leads to cytostatic agents with activity against drug resistant cancer cells and capable of pyrrolylation of primary amines.
Eur J Med Chem, 2015 Oct 20 , 103 (226-37).

37

Tan X et al. [Molecular genetic study of a family featuring cardiac conduction block].
Zhonghua Yi Xue Yi Chuan Xue Za Zhi, 2015 Oct , 32 (661-4).

38

Torbergsen T et al. Painful cramps and giant myotonic discharges in a family with the Nav1.4-G1306A mutation.
Muscle Nerve, 2015 Oct , 52 (680-3).

39

Brett TJ CLCA1 and TMEM16A: the link towards a potential cure for airway diseases.
Expert Rev Respir Med, 2015 Oct , 9 (503-6).

40

Nguyen CT et al. Characterization of the Chloride Channel-Like, AtCLCg, Involved in Chloride Tolerance in Arabidopsis thaliana.
Plant Cell Physiol., 2015 Nov 9 , ().

41

Last NB et al. Functional Monomerization of a ClC-Type Fluoride Transporter.
J. Mol. Biol., 2015 Nov 6 , 427 (3607-12).

42

Yang B et al. Low expression of chloride channel accessory 1 predicts a poor prognosis in colorectal cancer.
Cancer, 2015 May 15 , 121 (1570-80).

43

Yoshinaga H et al. Phenotypic variability in childhood of skeletal muscle sodium channelopathies.
Pediatr. Neurol., 2015 May , 52 (504-8).

44

Li J et al. The cystic fibrosis transmembrane conductance regulator as a biomarker in non-small cell lung cancer.
Int. J. Oncol., 2015 May , 46 (2107-15).

45

Hanagasi HA et al. Secondary paroxysmal kinesigenic dyskinesia associated with CLCN2 gene mutation.
Parkinsonism Relat. Disord., 2015 May , 21 (544-6).

46

de la Fuente-Ortega E et al. BASOLATERAL SORTING OF CHLORIDE CHANNEL 2 IS MEDIATED BY INTERACTIONS BETWEEN A DILEUCINE MOTIF AND THE CLATHRIN ADAPTOR AP-1.
Mol. Biol. Cell, 2015 Mar 4 , ().

47

Pillai S et al. β-arrestin-1 mediates nicotine-induced metastasis through E2F1 target genes that modulate epithelial-mesenchymal transition.
Cancer Res., 2015 Mar 15 , 75 (1009-20).

48

Dietert K et al. Murine CLCA5 is uniquely expressed in distinct niches of airway epithelial cells.
Histochem. Cell Biol., 2015 Mar , 143 (277-87).

49

Medjber K et al. Role of nicotinic acetylcholine receptors in cell proliferation and tumour invasion in broncho-pulmonary carcinomas.
Lung Cancer, 2015 Mar , 87 (258-64).

50

Ni Y et al. PKD1 is downregulated in non-small cell lung cancer and mediates the feedback inhibition of mTORC1-S6K1 axis in response to phorbol ester.
Int. J. Biochem. Cell Biol., 2015 Mar , 60 (34-42).

51

Andrini O et al. ClC-K chloride channels: emerging pathophysiology of Bartter syndrome type 3.
Am. J. Physiol. Renal Physiol., 2015 Jun 15 , 308 (F1324-34).

52

Hiromatsu R et al. NF-κB-regulated transcriptional control of CLCA in a differentiated mouse keratinocyte line.
J. Dermatol. Sci., 2015 Jun , 78 (189-96).

53

Pohl M et al. Short-term functional adaptation of aquaporin-1 surface expression in the proximal tubule, a component of glomerulotubular balance.
J. Am. Soc. Nephrol., 2015 Jun , 26 (1269-78).

54

Wang Y et al. Characterization of 26 deletion CNVs reveals the frequent occurrence of micro-mutations within the breakpoint-flanking regions and frequent repair of double-strand breaks by templated insertions derived from remote genomic regions.
Hum. Genet., 2015 Jun , 134 (589-603).

55

Ge LS et al. Changes in tumor-antigen expression profile as human small-cell lung cancers progress.
Cancer Biol Med, 2015 Jun , 12 (96-105).

56

Dodds KN et al. Uterine Contractility in the Nonpregnant Mouse: Changes During the Estrous Cycle and Effects of Chloride Channel Blockade.
Biol. Reprod., 2015 Jun , 92 (141).

57

Wojciechowski D et al. Tryptophan Scanning Mutagenesis Identifies the Molecular Determinants of Distinct Barttin Functions.
J. Biol. Chem., 2015 Jul 24 , 290 (18732-43).

58

Wang H et al. ClC-3 chloride channel functions as a mechanically sensitive channel in osteoblasts.
Biochem. Cell Biol., 2015 Jul 13 , (1-8).

59

Steinke KV et al. Human CLC-K Channels Require Palmitoylation of Their Accessory Subunit Barttin to Be Functional.
J. Biol. Chem., 2015 Jul 10 , 290 (17390-400).

60

Musrap N et al. Comparative Proteomics of Ovarian Cancer Aggregate Formation Reveals an Increased Expression of Calcium-activated Chloride Channel Regulator 1 (CLCA1).
J. Biol. Chem., 2015 Jul 10 , 290 (17218-27).

61

Liu H et al. Prognostic value of purinergic P2X7 receptor expression in patients with hepatocellular carcinoma after curative resection.
Tumour Biol., 2015 Jul , 36 (5039-49).

62

Kurita T et al. The ClC-7 Chloride Channel Is Downregulated by Hypoosmotic Stress in Human Chondrocytes.
Mol. Pharmacol., 2015 Jul , 88 (113-20).

63

Saha S et al. A pH-independent DNA nanodevice for quantifying chloride transport in organelles of living cells.
Nat Nanotechnol, 2015 Jul , 10 (645-51).

64

Jentsch TJ Discovery of CLC transport proteins: Cloning, structure, function and pathophysiology.
J. Physiol. (Lond.), 2015 Jan 15 , ().

65

Greenlee MM et al. Prolactin stimulates sodium and chloride ion channels in A6 renal epithelial cells.
Am. J. Physiol. Renal Physiol., 2015 Jan 13 , (ajprenal.00270.2014).

66

Zaika O et al. IGF-1 and insulin exert opposite actions on ClC-K2 activity in the cortical collecting ducts.
Am. J. Physiol. Renal Physiol., 2015 Jan 1 , 308 (F39-48).

67

Traister RS et al. Phenotypic and genotypic association of epithelial IL1RL1 to human TH2-like asthma.
J. Allergy Clin. Immunol., 2015 Jan , 135 (92-9).

68

Dubey M et al. Mice with megalencephalic leukoencephalopathy with cysts: a developmental angle.
Ann. Neurol., 2015 Jan , 77 (114-31).

69

Skov M et al. Extracellular magnesium and calcium reduce myotonia in isolated ClC-1 chloride channel-inhibited human muscle.
Muscle Nerve, 2015 Jan , 51 (65-71).

70

Capurro V et al. Functional analysis of acid-activated Cl⁻ channels: properties and mechanisms of regulation.
Biochim. Biophys. Acta, 2015 Jan , 1848 (105-14).

71

Jentsch TJ Discovery of CLC transport proteins: cloning, structure, function and pathophysiology.
J. Physiol. (Lond.), 2015 Feb 19 , ().

72

Jia Y et al. Loss of Clcc1 results in ER stress, misfolded protein accumulation, and neurodegeneration.
J. Neurosci., 2015 Feb 18 , 35 (3001-9).

73

Catalán MA et al. A fluid secretion pathway unmasked by acinar-specific Tmem16A gene ablation in the adult mouse salivary gland.
Proc. Natl. Acad. Sci. U.S.A., 2015 Feb 17 , 112 (2263-8).

74

Xu B et al. Chloride channel-3 promotes tumor metastasis by regulating membrane ruffling and is associated with poor survival.
Oncotarget, 2015 Feb 10 , 6 (2434-50).

75

Pereira NL et al. Circulating atrial natriuretic peptide genetic association study identifies a novel gene cluster associated with stroke in whites.
Circ Cardiovasc Genet, 2015 Feb , 8 (141-9).

76

Hong S et al. CLC-3 channels in cancer (review).
Oncol. Rep., 2015 Feb , 33 (507-14).

77

Stölting G et al. Carboxyl-terminal Truncations of ClC-Kb Abolish Channel Activation by Barttin Via Modified Common Gating and Trafficking.
J. Biol. Chem., 2015 Dec 18 , 290 (30406-16).

78

Grant J et al. A Novel Mechanism of pH Buffering in C. elegans Glia: Bicarbonate Transport via the Voltage-Gated ClC Cl- Channel CLH-1.
J. Neurosci., 2015 Dec 16 , 35 (16377-97).

79

Slaats GG et al. Screen-based identification and validation of four new ion channels as regulators of renal ciliogenesis.
J. Cell. Sci., 2015 Dec 15 , 128 (4550-9).

80

Bai ZH et al. [Effect of Electroacupuncture Stimulation of "Neiguan" (PC 6) on Expression of Myocardial Chloride Channel-related Genes, PKC and PKG Proteins in Myocardial Ischemia Rats].
Zhen Ci Yan Jiu, 2015 Dec , 40 (439-43).

81

Jian S et al. [Clinical and genetic analysis of Dent disease in 4 Chinese children].
Zhongguo Dang Dai Er Ke Za Zhi, 2015 Dec , 17 (1261-6).

82

Nanami M et al. ENaC inhibition stimulates HCl secretion in the mouse cortical collecting duct. I. Stilbene-sensitive Cl- secretion.
Am. J. Physiol. Renal Physiol., 2015 Aug 1 , 309 (F251-8).

83

Gaurav R et al. Chloride Channel 3 Channels in the Activation and Migration of Human Blood Eosinophils in Allergic Asthma.
Am. J. Respir. Cell Mol. Biol., 2015 Aug , 53 (235-45).

84

Mansour-Hendili L et al. Mutation Update of the CLCN5 Gene Responsible for Dent Disease 1.
Hum. Mutat., 2015 Aug , 36 (743-52).

85

Wen X et al. Dental and Cranial Pathologies in Mice Lacking the Cl(-) /H(+) -Exchanger ClC-7.
Anat Rec (Hoboken), 2015 Aug , 298 (1502-8).

86

Pérez-Rius C et al. Identification and characterization of the zebrafish ClC-2 chloride channel orthologs.
Pflugers Arch., 2015 Aug , 467 (1769-81).

87

Lee A et al. Chloride channel ClC-5 binds to aspartyl aminopeptidase to regulate renal albumin endocytosis.
Am. J. Physiol. Renal Physiol., 2015 Apr 1 , 308 (F784-92).

88

Li H et al. Nicotine induces resistance to erlotinib via cross-talk between α 1 nAChR and EGFR in the non-small cell lung cancer xenograft model.
Lung Cancer, 2015 Apr , 88 (1-8).

89

Togashi Y et al. Chronic nicotine exposure mediates resistance to EGFR-TKI in EGFR-mutated lung cancer via an EGFR signal.
Lung Cancer, 2015 Apr , 88 (16-23).

90

Bugiardini E et al. SCN4A mutation as modifying factor of myotonic dystrophy type 2 phenotype.
Neuromuscul. Disord., 2015 Apr , 25 (301-7).

91

Alonso A et al. Identification of risk loci for Crohn's disease phenotypes using a genome-wide association study.
Gastroenterology, 2015 Apr , 148 (794-805).

92

Zhang WW et al. MhNCED3, a gene encoding 9-cis-epoxycarotenoid dioxygenase in Malus hupehensis Rehd., enhances plant tolerance to Cl- stress by reducing Cl- accumulation.
Plant Physiol. Biochem., 2015 Apr , 89 (85-91).

93

Cannon SC Channelopathies of skeletal muscle excitability.
Compr Physiol, 2015 Apr , 5 (761-90).

94

Liu H et al. Upregulation of the inwardly rectifying potassium channel Kir2.1 (KCNJ2) modulates multidrug resistance of small-cell lung cancer under the regulation of miR-7 and the Ras/MAPK pathway.
Mol. Cancer, 2015 , 14 (59).

95

Yamamoto T et al. Single nucleotide variations in CLCN6 identified in patients with benign partial epilepsies in infancy and/or febrile seizures.
PLoS ONE, 2015 , 10 (e0118946).

96

Ruiz-Lafuente N et al. IL-4 Up-Regulates MiR-21 and the MiRNAs Hosted in the CLCN5 Gene in Chronic Lymphocytic Leukemia.
PLoS ONE, 2015 , 10 (e0124936).

97

Zhao B et al. 4,4'-Diisothiocyanostilbene-2,2'-disulfonic Acid (DIDS) Ameliorates Ischemia-Hypoxia-Induced White Matter Damage in Neonatal Rats through Inhibition of the Voltage-Gated Chloride Channel ClC-2.
Int J Mol Sci, 2015 , 16 (10457-69).

98

Imbrici P et al. ClC-1 chloride channels: state-of-the-art research and future challenges.
Front Cell Neurosci, 2015 , 9 (156).

99

Brignone MS et al. MLC1 protein: a likely link between leukodystrophies and brain channelopathies.
Front Cell Neurosci, 2015 , 9 (66).

100

Ronstedt K et al. Impaired surface membrane insertion of homo- and heterodimeric human muscle chloride channels carrying amino-terminal myotonia-causing mutations.
Sci Rep, 2015 , 5 (15382).

101

Pottosin I et al. Ion Channels in Native Chloroplast Membranes: Challenges and Potential for Direct Patch-Clamp Studies.
Front Physiol, 2015 , 6 (396).

102

Nikolaidou T et al. Congestive Heart Failure Leads to Prolongation of the PR Interval and Atrioventricular Junction Enlargement and Ion Channel Remodelling in the Rabbit.
PLoS ONE, 2015 , 10 (e0141452).

103

Basilio D et al. A Proteoliposome-Based Efflux Assay to Determine Single-molecule Properties of Cl- Channels and Transporters.
J Vis Exp, 2015 , ().

104

Sala-Rabanal M et al. Secreted CLCA1 modulates TMEM16A to activate Ca(2+)-dependent chloride currents in human cells.
Elife, 2015 , 4 ().

105

Du S et al. ClC-3 chloride channel modulates the proliferation and migration of osteosarcoma cells via AKT/GSK3β signaling pathway.
Int J Clin Exp Pathol, 2015 , 8 (1622-30).

106

Du YH et al. Chloride Channels - New Targets for the Prevention of Stroke.
Curr Vasc Pharmacol, 2015 , 13 (441-8).

107

Chen YA et al. The Cullin 4A/B-DDB1-Cereblon E3 Ubiquitin Ligase Complex Mediates the Degradation of CLC-1 Chloride Channels.
Sci Rep, 2015 , 5 (10667).

108

Erickson NA et al. The Goblet Cell Protein Clca1 (Alias mClca3 or Gob-5) Is Not Required for Intestinal Mucus Synthesis, Structure and Barrier Function in Naive or DSS-Challenged Mice.
PLoS ONE, 2015 , 10 (e0131991).

109

Zhan ZY et al. Over-expression of Orai1 mediates cell proliferation and associates with poor prognosis in human non-small cell lung carcinoma.
Int J Clin Exp Pathol, 2015 , 8 (5080-8).

110

Pan F et al. High glucose inhibits ClC-2 chloride channels and attenuates cell migration of rat keratinocytes.
Drug Des Devel Ther, 2015 , 9 (4779-91).

111

Nighot MP et al. Genetic Ablation of the ClC-2 Cl- Channel Disrupts Mouse Gastric Parietal Cell Acid Secretion.
PLoS ONE, 2015 , 10 (e0138174).

112

Plog S et al. Naturally Occurring Deletion Mutants of the Pig-Specific, Intestinal Crypt Epithelial Cell Protein CLCA4b without Apparent Phenotype.
PLoS ONE, 2015 , 10 (e0140050).

113

Turner A et al. Development and validation of a high throughput, closed tube method for the determination of haemoglobin alpha gene (HBA1 and HBA2) numbers by gene ratio assay copy enumeration-PCR (GRACE-PCR).
BMC Med. Genet., 2015 , 16 (115).

114

Ge Y et al. Novel Molecular Regulators of Tumor Necrosis Factor-Related Apoptosis-Inducing Ligand (TRAIL)-Induced Apoptosis in NSCLC Cells.
Clin. Lab., 2015 , 61 (1855-63).

115

Milosavljevic N et al. Functional Characterization of Na+/H+ Exchangers of Intracellular Compartments Using Proton-killing Selection to Express Them at the Plasma Membrane.
J Vis Exp, 2015 , ().

116

Wang YF et al. Molecular Physiology of an Extra-renal Cl(-) Uptake Mechanism for Body Fluid Cl(-) Homeostasis.
Int. J. Biol. Sci., 2015 , 11 (1190-203).

117

Jena BP Porosome in Cystic Fibrosis.
Discoveries (Craiova), 2014 Jul-Sep , 2 ().

118

Cabrero P et al. Chloride channels in stellate cells are essential for uniquely high secretion rates in neuropeptide-stimulated Drosophila diuresis.
Proc. Natl. Acad. Sci. U.S.A., 2014 Sep 30 , 111 (14301-6).

119

Di Bella D et al. Subclinical leukodystrophy and infertility in a man with a novel homozygous CLCN2 mutation.
Neurology, 2014 Sep 23 , 83 (1217-8).

120

Jeworutzki E et al. GlialCAM, a CLC-2 Cl(-) channel subunit, activates the slow gate of CLC chloride channels.
Biophys. J., 2014 Sep 2 , 107 (1105-16).

121

Grieschat M et al. Multiple discrete transitions underlie voltage-dependent activation in CLC Cl(-)/H(+) antiporters.
Biophys. J., 2014 Sep 16 , 107 (L13-5).

122

Fahlke C Behind the scenes of CLC gating: deriving the voltage dependence of membrane proteins by admittance measurements.
Biophys. J., 2014 Sep 16 , 107 (1261-2).

123

Domingue JC et al. HEK-293 cells expressing the cystic fibrosis transmembrane conductance regulator (CFTR): a model for studying regulation of Cl- transport.
Physiol Rep, 2014 Sep 1 , 2 ().

124

Cuppoletti J et al. Differentiation between human ClC-2 and CFTR Cl- channels with pharmacological agents.
Am. J. Physiol., Cell Physiol., 2014 Sep 1 , 307 (C479-92).

125

Licchetta L et al. Limbic encephalitis with anti-GAD antibodies and Thomsen myotonia: a casual or causal association?
Epileptic Disord, 2014 Sep , 16 (362-5).

126

Andrini O et al. CLCNKB mutations causing mild Bartter syndrome profoundly alter the pH and Ca2+ dependence of ClC-Kb channels.
Pflugers Arch., 2014 Sep , 466 (1713-23).

127

Xie J et al. Identification of atomic-level mechanisms for gas-phase X- + CH3Y SN2 reactions by combined experiments and simulations.
Acc. Chem. Res., 2014 Oct 21 , 47 (2960-9).

128

Riisager A et al. Determination of cable parameters in skeletal muscle fibres during repetitive firing of action potentials.
J. Physiol. (Lond.), 2014 Oct 15 , 592 (4417-29).

129

Cozzoli A et al. Angiotensin II modulates mouse skeletal muscle resting conductance to chloride and potassium ions and calcium homeostasis via the AT1 receptor and NADPH oxidase.
Am. J. Physiol., Cell Physiol., 2014 Oct 1 , 307 (C634-47).

130

Huang LY et al. ClC-3 chloride channel/antiporter defect contributes to inflammatory bowel disease in humans and mice.
Gut, 2014 Oct , 63 (1587-95).

131

Li X et al. [Genetic analysis of a novel mutation resulting in autosomal dominant osteopetrosis II].
Zhonghua Yi Xue Yi Chuan Xue Za Zhi, 2014 Oct , 31 (612-4).

132

Imbrici P et al. Targeting kidney CLC-K channels: pharmacological profile in a human cell line versus Xenopus oocytes.
Biochim. Biophys. Acta, 2014 Oct , 1838 (2484-91).

133

Yoo SS et al. Unmethylation of the CHRNB4 gene is an unfavorable prognostic factor in non-small cell lung cancer.
Lung Cancer, 2014 Oct , 86 (85-90).

134

Cramer MT et al. Expanding the phenotype of proteinuria in Dent disease. A case series.
Pediatr. Nephrol., 2014 Oct , 29 (2051-4).

135

Guéguinou M et al. Lipid rafts, KCa/ClCa/Ca(2+) channel complexes and EGFR signaling: Novel targets to reduce tumor development by lipids?
Biochim. Biophys. Acta, 2014 Nov 4 , ().

136

Perumal D et al. Nicotinic acetylcholine receptors induce c-Kit ligand/Stem Cell Factor and promote stemness in an ARRB1/ β-arrestin-1 dependent manner in NSCLC.
Oncotarget, 2014 Nov 15 , 5 (10486-502).

137

Pusch M et al. ClC-5: Physiological role and biophysical mechanisms.
Cell Calcium, 2014 Nov 13 , ().

138

Hoche F et al. Novel N-terminal truncating CLCN1 mutation in severe Becker disease.
Muscle Nerve, 2014 Nov , 50 (866-7).

139

Huang YY et al. ClC-3 deficiency protects preadipocytes against apoptosis induced by palmitate in vitro and in type 2 diabetes mice.
Apoptosis, 2014 Nov , 19 (1559-70).

140

Furby A et al. Heterozygous CLCN1 mutations can modulate phenotype in sodium channel myotonia.
Neuromuscul. Disord., 2014 Nov , 24 (953-9).

141

Park E et al. Muscle involvement in Dent disease 2.
Pediatr. Nephrol., 2014 Nov , 29 (2127-32).

142

Pritchard HA et al. Inhibitory role of phosphatidylinositol 4,5 bisphosphate on TMEM16A encoded calcium-activated chloride channels in rat pulmonary artery.
Br. J. Pharmacol., 2014 May 19 , ().

143

Basilio D et al. Conformational changes required for H(+)/Cl(-) exchange mediated by a CLC transporter.
Nat. Struct. Mol. Biol., 2014 May , 21 (456-63).

144

Warsi J et al. Downregulation of chloride channel ClC-2 by Janus kinase 3.
J. Membr. Biol., 2014 May , 247 (387-93).

145

Wang Y et al. Neuronal acetylcholine receptor subunit alpha-9 (CHRNA9) polymorphisms are associated with NSCLC risk in a Chinese population.
Med. Oncol., 2014 May , 31 (932).

146

Ulzi G et al. In vitro analysis of splice site mutations in the CLCN1 gene using the minigene assay.
Mol. Biol. Rep., 2014 May , 41 (2865-74).

147

de Pablos AL et al. Severe manifestation of Bartter syndrome Type IV caused by a novel insertion mutation in the BSND gene.
Clin. Nephrol., 2014 May , 81 (363-8).

148

Dabby R et al. Myotonia in DNM2-related centronuclear myopathy.
J Neural Transm, 2014 May , 121 (549-53).

149

Yan Y et al. Increase in hypotonic stress-induced endocytic activity in macrophages via ClC-3.
Mol. Cells, 2014 May , 37 (418-25).

150

Moreno-Galindo EG et al. The principal conductance in Giardia lamblia trophozoites possesses functional properties similar to the mammalian ClC-2 current.
Pflugers Arch., 2014 May , 466 (915-24).

151

Yan F et al. Interleukin-13-induced MUC5AC expression is regulated by a PI3K-NFAT3 pathway in mouse tracheal epithelial cells.
Biochem. Biophys. Res. Commun., 2014 Mar 28 , 446 (49-53).

152

Ta VT et al. Reusable floating-electrode sensor for the quantitative electrophysiological monitoring of a nonadherent cell.
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