PubMed 21401653

Referenced in Channelpedia wiki pages of: none

Automatically associated channels: KCNQ1 , Kir6.2 , Kv7.1

Title: Fetal and neonatal presentation of long QT syndrome.

Authors: Rukmini Komarlu, Lee Beerman, David Freeman, Gaurav Arora

Journal, date & volume: Pacing Clin Electrophysiol, 2012 Apr , 35, e87-90

PubMed link:

This report describes a fetus presenting with intrauterine tachycardia and hydrops fetalis. Soon after birth the neonate was noted to be in torsades de pointes that responded dramatically to medical management. Long QT syndrome (LQTS) was diagnosed on electrocardiogram obtained soon after birth. The prognosis is poor when LQTS presents in utero or during the first week of life. However, our infant did well with medical management and has remained free of arrhythmias at follow-up.