Referenced in: none

Automatically associated channels: Kir2.1

Title: Sudden cardiac death in Andersen-Tawil syndrome.

Authors: Stefan Peters, Eric Schulze-Bahr, Susan P Etheridge, Martin Tristani-Firouzi

Journal, date & volume: , 2007 Mar , 9, 162-6

PubMed link: http://www.ncbi.nlm.nih.gov/pubmed/17272325

Abstract
Andersen-Tawil syndrome (ATS) is an autosomal dominant or sporadic disorder characterized by periodic paralysis, dysmorphic features, and ventricular arrhythmias. Although ventricular tachycardia burden is quite high sudden cardiac death in ATS is rare. We describe a case with sudden cardiac death due to electrical storm a few days after ICD implantation in KCNJ2 mutation-negative ATS.