Channelpedia

ClvC4 Channel

2001 automatically matched literature references

2

Wang Q et al. Local coupling of TRPC6 to ANO1/TMEM16A channels in smooth muscle cells amplifies vasoconstriction in cerebral arteries.
Am. J. Physiol., Cell Physiol., 2016 May 4 , (ajpcell.00092.2016).

3

Zaika O et al. New perspective of ClC-Kb/2 Cl- channel physiology in the distal renal tubule.
Am. J. Physiol. Renal Physiol., 2016 May 15 , 310 (F923-30).

5

Perrouin Verbe MA et al. Expression of store-operated channel components in prostate cancer: the prognostic paradox.
Hum. Pathol., 2016 Mar , 49 (77-82).

9

De Jesús-Pérez JJ et al. Gating the glutamate gate of CLC-2 chloride channel by pore occupancy.
J. Gen. Physiol., 2016 Jan , 147 (25-37).

20

Arcangeli A et al. Novel perspectives in cancer therapy: Targeting ion channels.
Drug Resist. Updat., 2015 Jul-Aug , 21-22 (11-9).

21

22

Lopez HU et al. Whole-Exome Sequencing Reveals CLCNKB Mutations in a Case of Sudden Unexpected Infant Death.
Pediatr. Dev. Pathol., 2015 Jul-Aug , 18 (324-6).

24

Bulk E et al. Epigenetic dysregulation of KCa 3.1 channels induces poor prognosis in lung cancer.
Int. J. Cancer, 2015 Sep 15 , 137 (1306-17).

25

Fong P Twenty-five years of CLC chloride transport proteins.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4083-4).

26

Accardi A Structure and gating of CLC channels and exchangers.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4129-38).

30

Devuyst O et al. Chloride transporters and receptor-mediated endocytosis in the renal proximal tubule.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4151-64).

31

Barrallo-Gimeno A et al. Regulatory-auxiliary subunits of CLC chloride channel-transport proteins.
J. Physiol. (Lond.), 2015 Sep 15 , 593 (4111-27).

34

Dogan Onugoren M et al. Limbic encephalitis due to GABAB and AMPA receptor antibodies: a case series.
J. Neurol. Neurosurg. Psychiatr., 2015 Sep , 86 (965-72).

37

Tan X et al. [Molecular genetic study of a family featuring cardiac conduction block].
Zhonghua Yi Xue Yi Chuan Xue Za Zhi, 2015 Oct , 32 (661-4).

38

39

Brett TJ CLCA1 and TMEM16A: the link towards a potential cure for airway diseases.
Expert Rev Respir Med, 2015 Oct , 9 (503-6).

41

Last NB et al. Functional Monomerization of a ClC-Type Fluoride Transporter.
J. Mol. Biol., 2015 Nov 6 , 427 (3607-12).

44

Yoshinaga H et al. Phenotypic variability in childhood of skeletal muscle sodium channelopathies.
Pediatr. Neurol., 2015 May , 52 (504-8).

45

Hanagasi HA et al. Secondary paroxysmal kinesigenic dyskinesia associated with CLCN2 gene mutation.
Parkinsonism Relat. Disord., 2015 May , 21 (544-6).

48

Dietert K et al. Murine CLCA5 is uniquely expressed in distinct niches of airway epithelial cells.
Histochem. Cell Biol., 2015 Mar , 143 (277-87).

51

Andrini O et al. ClC-K chloride channels: emerging pathophysiology of Bartter syndrome type 3.
Am. J. Physiol. Renal Physiol., 2015 Jun 15 , 308 (F1324-34).

52

55

Hiromatsu R et al. NF-κB-regulated transcriptional control of CLCA in a differentiated mouse keratinocyte line.
J. Dermatol. Sci., 2015 Jun , 78 (189-96).

57

Wojciechowski D et al. Tryptophan Scanning Mutagenesis Identifies the Molecular Determinants of Distinct Barttin Functions.
J. Biol. Chem., 2015 Jul 24 , 290 (18732-43).

58

Wang H et al. ClC-3 chloride channel functions as a mechanically sensitive channel in osteoblasts.
Biochem. Cell Biol., 2015 Jul 13 , (1-8).

59

Steinke KV et al. Human CLC-K Channels Require Palmitoylation of Their Accessory Subunit Barttin to Be Functional.
J. Biol. Chem., 2015 Jul 10 , 290 (17390-400).

61

Kurita T et al. The ClC-7 Chloride Channel Is Downregulated by Hypoosmotic Stress in Human Chondrocytes.
Mol. Pharmacol., 2015 Jul , 88 (113-20).

65

Greenlee MM et al. Prolactin stimulates sodium and chloride ion channels in A6 renal epithelial cells.
Am. J. Physiol. Renal Physiol., 2015 Jan 13 , (ajprenal.00270.2014).

66

Zaika O et al. IGF-1 and insulin exert opposite actions on ClC-K2 activity in the cortical collecting ducts.
Am. J. Physiol. Renal Physiol., 2015 Jan 1 , 308 (F39-48).

67

Dubey M et al. Mice with megalencephalic leukoencephalopathy with cysts: a developmental angle.
Ann. Neurol., 2015 Jan , 77 (114-31).

68

Capurro V et al. Functional analysis of acid-activated Cl⁻ channels: properties and mechanisms of regulation.
Biochim. Biophys. Acta, 2015 Jan , 1848 (105-14).

69

Traister RS et al. Phenotypic and genotypic association of epithelial IL1RL1 to human TH2-like asthma.
J. Allergy Clin. Immunol., 2015 Jan , 135 (92-9).

73

Catalán MA et al. A fluid secretion pathway unmasked by acinar-specific Tmem16A gene ablation in the adult mouse salivary gland.
Proc. Natl. Acad. Sci. U.S.A., 2015 Feb 17 , 112 (2263-8).

75

Hong S et al. CLC-3 channels in cancer (review).
Oncol. Rep., 2015 Feb , 33 (507-14).

81

Jian S et al. [Clinical and genetic analysis of Dent disease in 4 Chinese children].
Zhongguo Dang Dai Er Ke Za Zhi, 2015 Dec , 17 (1261-6).

82

83

Gaurav R et al. Chloride Channel 3 Channels in the Activation and Migration of Human Blood Eosinophils in Allergic Asthma.
Am. J. Respir. Cell Mol. Biol., 2015 Aug , 53 (235-45).

84

Mansour-Hendili L et al. Mutation Update of the CLCN5 Gene Responsible for Dent Disease 1.
Hum. Mutat., 2015 Aug , 36 (743-52).

85

Wen X et al. Dental and Cranial Pathologies in Mice Lacking the Cl(-) /H(+) -Exchanger ClC-7.
Anat Rec (Hoboken), 2015 Aug , 298 (1502-8).

86

Pérez-Rius C et al. Identification and characterization of the zebrafish ClC-2 chloride channel orthologs.
Pflugers Arch., 2015 Aug , 467 (1769-81).

87

Lee A et al. Chloride channel ClC-5 binds to aspartyl aminopeptidase to regulate renal albumin endocytosis.
Am. J. Physiol. Renal Physiol., 2015 Apr 1 , 308 (F784-92).

88

Cannon SC Channelopathies of skeletal muscle excitability.
Compr Physiol, 2015 Apr , 5 (761-90).

89

93

Bugiardini E et al. SCN4A mutation as modifying factor of myotonic dystrophy type 2 phenotype.
Neuromuscul. Disord., 2015 Apr , 25 (301-7).

97

Imbrici P et al. ClC-1 chloride channels: state-of-the-art research and future challenges.
Front Cell Neurosci, 2015 , 9 (156).

99

Brignone MS et al. MLC1 protein: a likely link between leukodystrophies and brain channelopathies.
Front Cell Neurosci, 2015 , 9 (66).

116

Du YH et al. Chloride Channels - New Targets for the Prevention of Stroke.
Curr Vasc Pharmacol, 2015 , 13 (441-8).

117

Jena BP Porosome in Cystic Fibrosis.
Discoveries (Craiova), 2014 Jul-Sep , 2 ().

119

120

Jeworutzki E et al. GlialCAM, a CLC-2 Cl(-) channel subunit, activates the slow gate of CLC chloride channels.
Biophys. J., 2014 Sep 2 , 107 (1105-16).

124

Cuppoletti J et al. Differentiation between human ClC-2 and CFTR Cl- channels with pharmacological agents.
Am. J. Physiol., Cell Physiol., 2014 Sep 1 , 307 (C479-92).

125

128

130

Li X et al. [Genetic analysis of a novel mutation resulting in autosomal dominant osteopetrosis II].
Zhonghua Yi Xue Yi Chuan Xue Za Zhi, 2014 Oct , 31 (612-4).

131

Imbrici P et al. Targeting kidney CLC-K channels: pharmacological profile in a human cell line versus Xenopus oocytes.
Biochim. Biophys. Acta, 2014 Oct , 1838 (2484-91).

134

Cramer MT et al. Expanding the phenotype of proteinuria in Dent disease. A case series.
Pediatr. Nephrol., 2014 Oct , 29 (2051-4).

137

Pusch M et al. ClC-5: Physiological role and biophysical mechanisms.
Cell Calcium, 2014 Nov 13 , ().

138

Hoche F et al. Novel N-terminal truncating CLCN1 mutation in severe Becker disease.
Muscle Nerve, 2014 Nov , 50 (866-7).

140

Furby A et al. Heterozygous CLCN1 mutations can modulate phenotype in sodium channel myotonia.
Neuromuscul. Disord., 2014 Nov , 24 (953-9).

141

Park E et al. Muscle involvement in Dent disease 2.
Pediatr. Nephrol., 2014 Nov , 29 (2127-32).

143

144

Basilio D et al. Conformational changes required for H(+)/Cl(-) exchange mediated by a CLC transporter.
Nat. Struct. Mol. Biol., 2014 May , 21 (456-63).

146

Warsi J et al. Downregulation of chloride channel ClC-2 by Janus kinase 3.
J. Membr. Biol., 2014 May , 247 (387-93).

147

Ulzi G et al. In vitro analysis of splice site mutations in the CLCN1 gene using the minigene assay.
Mol. Biol. Rep., 2014 May , 41 (2865-74).

148

Dabby R et al. Myotonia in DNM2-related centronuclear myopathy.
J Neural Transm, 2014 May , 121 (549-53).

151

153

Stölting G et al. ClC-1 and ClC-2 form hetero-dimeric channels with novel protopore functions.
Pflugers Arch., 2014 Mar 19 , ().

163

Tan SV et al. Chloride channels in myotonia congenita assessed by velocity recovery cycles.
Muscle Nerve, 2014 Jun , 49 (845-57).

171

176

Peters MC et al. Measures of gene expression in sputum cells can identify TH2-high and TH2-low subtypes of asthma.
J. Allergy Clin. Immunol., 2014 Feb , 133 (388-94).

178

Chiang WF et al. Hypokalemic paralysis in a middle-aged female with classic Bartter syndrome.
Clin. Nephrol., 2014 Feb , 81 (146-50).

179

187

McCarthy NS et al. Two further blood pressure loci identified in ion channel genes with a gene-centric approach.
Circ Cardiovasc Genet, 2014 Dec , 7 (873-9).

189

Cardani R et al. Progression of muscle histopathology but not of spliceopathy in myotonic dystrophy type 2.
Neuromuscul. Disord., 2014 Dec , 24 (1042-53).

193

Kassardjian CD et al. Coexistence of DMPK gene expansion and CLCN1 missense mutation in the same patient.
Neurogenetics, 2014 Aug , 15 (213-4).

194

Ji LN et al. A novel CLCN5 mutation in a Chinese boy with Dent's disease.
World J Pediatr, 2014 Aug , 10 (275-7).

195

Brammer AE et al. F-/Cl- selectivity in CLCF-type F-/H+ antiporters.
J. Gen. Physiol., 2014 Aug , 144 (129-36).

197

Needham M et al. The role of K+ and Cl- channels in the regulation of retinal arteriolar tone and blood flow.
Invest. Ophthalmol. Vis. Sci., 2014 Apr , 55 (2157-65).

198

Richardson RC et al. Truncating CLCN1 mutations in myotonia congenita: variable patterns of inheritance.
Muscle Nerve, 2014 Apr , 49 (593-600).

200

Passeri E et al. Asymptomatic myotonia congenita unmasked by severe hypothyroidism.
Neuromuscul. Disord., 2014 Apr , 24 (365-7).

202

206

El-Ghlban S et al. Chlorotoxin-Fc fusion inhibits release of MMP-2 from pancreatic cancer cells.
Biomed Res Int, 2014 , 2014 (152659).

207

Pusch M et al. Thermal sensitivity of CLC and TMEM16 chloride channels and transporters.
Curr Top Membr, 2014 , 74 (213-31).

208

Gandolfi B et al. A novel mutation in CLCN1 associated with feline myotonia congenita.
PLoS ONE, 2014 , 9 (e109926).

210

Stölting G et al. CLC channel function and dysfunction in health and disease.
Front Physiol, 2014 , 5 (378).

214

Platt C et al. Dent's disease complicated by an acute Budd-Chiari syndrome.
BMJ Case Rep, 2014 , 2014 ().

215

Bi MM et al. Chloride channelopathies of ClC-2.
Int J Mol Sci, 2014 , 15 (218-49).

218

Boldrini L et al. P2X7 protein expression and polymorphism in non-small cell lung cancer (NSCLC).
J Negat Results Biomed, 2014 , 13 (16).

222

Warsi J et al. Regulation of ClC-2 activity by SPAK and OSR1.
Kidney Blood Press. Res., 2014 , 39 (378-87).

223

225

Guo W et al. The roles of anion channels in Arabidopsis immunity.
Plant Signal Behav, 2014 , 9 (e29230).

229

Bulley S et al. Cl(-) channels in smooth muscle cells.
Pflugers Arch., 2013 Sep 28 , ().

230

Duan X Ion Channels, Channelopathies, and Tooth Formation.
J. Dent. Res., 2013 Sep 27 , ().

233

239

Wang HW et al. Effect of CLC-2 on the cytoskeleton in human trabecular meshwork cells.
Mol Med Rep, 2013 Oct , 8 (1099-105).

242

Stölting G et al. Regulation of ClC-2 gating by intracellular ATP.
Pflugers Arch., 2013 Oct , 465 (1423-37).

243

Lucchiari S et al. Clinical evaluation and cellular electrophysiology of a recessive CLCN1 patient.
J. Physiol. Pharmacol., 2013 Oct , 64 (669-78).

245

Lim HH et al. Fluoride-dependent interruption of the transport cycle of a CLC Cl-/H+ antiporter.
Nat. Chem. Biol., 2013 Nov , 9 (721-5).

246

L'Hoste S et al. Characterization of the mouse ClC-K1/Barttin chloride channel.
Biochim. Biophys. Acta, 2013 Nov , 1828 (2399-409).

249

251

Waters CW et al. Huntington disease skeletal muscle is hyperexcitable owing to chloride and potassium channel dysfunction.
Proc. Natl. Acad. Sci. U.S.A., 2013 May 28 , 110 (9160-5).

254

Thompson EM et al. Inhibition of SUR1 decreases the vascular permeability of cerebral metastases.
Neoplasia, 2013 May , 15 (535-43).

257

Schiffhauer ES et al. Dual activation of CFTR and CLCN2 by lubiprostone in murine nasal epithelia.
Am. J. Physiol. Lung Cell Mol. Physiol., 2013 Mar 1 , 304 (L324-31).

258

259

Lakraj AA et al. Novel mutations in the CLCN1 gene of myotonia congenita: 2 case reports.
Yale J Biol Med, 2013 Mar , 86 (101-6).

260

Borges AS et al. Clinical and molecular study of a new form of hereditary myotonia in Murrah water buffalo.
Neuromuscul. Disord., 2013 Mar , 23 (206-13).

261

Zhang H et al. The ClC-3 chloride channel protein is a downstream target of cyclin D1 in nasopharyngeal carcinoma cells.
Int. J. Biochem. Cell Biol., 2013 Mar , 45 (672-83).

262

Duan X et al. Odontoblast-like MDPC-23 cells function as odontoclasts with RANKL/M-CSF induction.
Arch. Oral Biol., 2013 Mar , 58 (272-8).

264

Cuddapah VA et al. Calcium entry via TRPC1 channels activates chloride currents in human glioma cells.
Cell Calcium, 2013 Mar , 53 (187-94).

266

Gokel GW et al. Synthetic Ion Channels: From Pores to Biological Applications.
Acc. Chem. Res., 2013 Jun 5 , ().

267

268

270

Ishida Y et al. A model of lysosomal pH regulation.
J. Gen. Physiol., 2013 Jun , 141 (705-20).

272

Cho HY et al. Translational read-through of a nonsense mutation causing Bartter syndrome.
J. Korean Med. Sci., 2013 Jun , 28 (821-6).

274

275

276

Skov M et al. Extracellular magnesium and calcium reduce myotonia in ClC-1 inhibited rat muscle.
Neuromuscul. Disord., 2013 Jun , 23 (489-502).

279

Gradogna A et al. Alkaline pH block of CLC-K kidney chloride channels mediated by a pore lysine residue.
Biophys. J., 2013 Jul 2 , 105 (80-90).

280

Denton JS et al. Invited Review - Novel Diuretic Targets.
Am. J. Physiol. Renal Physiol., 2013 Jul 17 , ().

282

284

Huijbers MG et al. Antibodies to active zone protein ERC1 in Lambert-Eaton myasthenic syndrome.
Hum. Immunol., 2013 Jul , 74 (849-51).

285

Bossus M et al. The ClC-3 chloride channel and osmoregulation in the European sea bass, Dicentrarchus labrax.
J. Comp. Physiol. B, Biochem. Syst. Environ. Physiol., 2013 Jul , 183 (641-62).

286

Cuddapah VA et al. Bradykinin-induced chemotaxis of human gliomas requires the activation of KCa3.1 and ClC-3.
J. Neurosci., 2013 Jan 23 , 33 (1427-40).

287

de Paoli FV et al. Relationship between membrane Cl- conductance and contractile endurance in isolated rat muscles.
J. Physiol. (Lond.), 2013 Jan 15 , 591 (531-45).

289

Ganapathi SB et al. Functional regulation of ClC-3 in the migration of vascular smooth muscle cells.
Hypertension, 2013 Jan , 61 (174-9).

290

Arnaiz I et al. Changing expression of chloride channels during preimplantation mouse development.
Reproduction, 2013 Jan , 145 (73-84).

292

Zhang YP et al. Chloride channels in stroke.
Acta Pharmacol. Sin., 2013 Jan , 34 (17-23).

294

Farmer LM et al. CLC-3 chloride channels moderate long-term potentiation at Schaffer collateral-CA1 synapses.
J. Physiol. (Lond.), 2013 Feb 15 , 591 (1001-15).

297

De Stefano S et al. A single point mutation reveals gating of the human ClC-5 Cl-/H+ antiporter.
J. Physiol. (Lond.), 2013 Dec 1 , 591 (5879-93).

299

Nighot P et al. Chloride channel ClC-2 is a key factor in the development of DSS-induced murine colitis.
Inflamm. Bowel Dis., 2013 Dec , 19 (2867-77).

305

Ochoa-de la Paz LD et al. Characterization of an outward rectifying chloride current of Xenopus tropicalis oocytes.
Biochim. Biophys. Acta, 2013 Aug , 1828 (1743-53).

306

Bollerslev J et al. Autosomal dominant osteopetrosis revisited: lessons from recent studies.
Eur. J. Endocrinol., 2013 Aug , 169 (R39-57).

307

Morrow JM et al. Muscle MRI reveals distinct abnormalities in genetically proven non-dystrophic myotonias.
Neuromuscul. Disord., 2013 Aug , 23 (637-46).

310

312

Garcia-Celma J et al. Functional characterization of a ClC transporter by solid-supported membrane electrophysiology.
J. Gen. Physiol., 2013 Apr , 141 (479-91).

314

Duan DD Phenomics of cardiac chloride channels.
Compr Physiol, 2013 Apr , 3 (667-92).

315

Matchkov VV et al. Transport and function of chloride in vascular smooth muscles.
J. Vasc. Res., 2013 , 50 (69-87).

317

Improgo MR et al. Nicotinic acetylcholine receptors mediate lung cancer growth.
Front Physiol, 2013 , 4 (251).

319

de Lima Marson FA et al. Genetic interaction of GSH metabolic pathway genes in cystic fibrosis.
BMC Med. Genet., 2013 , 14 (60).

321

Szewczyk KA et al. Distinctive subdomains in the resorbing surface of osteoclasts.
PLoS ONE, 2013 , 8 (e60285).

324

Hehir MK et al. Double trouble in a patient with myotonia.
BMJ Case Rep, 2013 , 2013 ().

325

Zanardi I et al. An optical assay of the transport activity of ClC-7.
Sci Rep, 2013 , 3 (1231).

326

328

333

Bennetts B et al. Molecular determinants of common gating of a ClC chloride channel.
Nat Commun, 2013 , 4 (2507).

334

García Castaño A et al. Genetics of type III Bartter syndrome in Spain, proposed diagnostic algorithm.
PLoS ONE, 2013 , 8 (e74673).

345

Song L et al. Antibody to mCLCA3 suppresses symptoms in a mouse model of asthma.
PLoS ONE, 2013 , 8 (e82367).

347

Ishiura S et al. [Myotonic dystrophy].
Rinsho Shinkeigaku, 2013 , 53 (1109-11).

349

Norimatsu Y et al. Lubiprostone activates CFTR, but not ClC-2, via the prostaglandin receptor (EP(4)).
Biochem. Biophys. Res. Commun., 2012 Sep 28 , 426 (374-9).

350

Stockbridge RB et al. Fluoride resistance and transport by riboswitch-controlled CLC antiporters.
Proc. Natl. Acad. Sci. U.S.A., 2012 Sep 18 , 109 (15289-94).

351

Nighot M et al. Gastro protective properties of the novel prostone SPI-8811 against acid-injured porcine mucosa.
World J. Gastroenterol., 2012 Sep 14 , 18 (4684-92).

354

Krücken J et al. Anthelmintic cyclcooctadepsipeptides: complex in structure and mode of action.
Trends Parasitol., 2012 Sep , 28 (385-94).

356

Choi YR et al. Synthetic chloride transporters with the binding mode observed in a ClC chloride channel.
Chem. Commun. (Camb.), 2012 Oct 25 , 48 (10346-8).

357

Miyazaki H et al. CLC anion channel regulatory phosphorylation and conserved signal transduction domains.
Biophys. J., 2012 Oct 17 , 103 (1706-18).

358

Ursu SF et al. ClC1 chloride channel in myotonic dystrophy type 2 and ClC1 splicing in vitro.
Acta Myol, 2012 Oct , 31 (144-53).

361

Phillips S et al. Surprises from an unusual CLC homolog.
Biophys. J., 2012 Nov 7 , 103 (L44-6).

362

Zanatta AP et al. Integrin participates in the effect of thyroxine on plasma membrane in immature rat testis.
Biochim. Biophys. Acta, 2012 Nov 5 , ().

364

Howery AE et al. A designed inhibitor of a CLC antiporter blocks function through a unique binding mode.
Chem. Biol., 2012 Nov 21 , 19 (1460-70).

367

Kang XL et al. Differences between femoral artery and vein smooth muscle cells in volume-regulated chloride channels.
Can. J. Physiol. Pharmacol., 2012 Nov , 90 (1516-26).

371

Zifarelli G et al. On the mechanism of gating charge movement of ClC-5, a human Cl(-)/H(+) antiporter.
Biophys. J., 2012 May 2 , 102 (2060-9).

372

374

Cesario A et al. Is α7-nAChR a possible target for lung cancer and malignant pleural mesothelioma treatment?
Curr Drug Targets, 2012 May , 13 (688-94).

376

Grieschat M et al. Glutamate 268 regulates transport probability of the anion/proton exchanger ClC-5.
J. Biol. Chem., 2012 Mar 9 , 287 (8101-9).

379

Urity VB et al. Architecture of kangaroo rat inner medulla: segmentation of descending thin limb of Henle's loop.
Am. J. Physiol. Regul. Integr. Comp. Physiol., 2012 Mar 15 , 302 (R720-6).

380

Weiss N Cross-talk between TRPML1 channel, lipids and lysosomal storage diseases.
Commun Integr Biol, 2012 Mar 1 , 5 (111-3).

381

Kondo M et al. Niflumic Acid inhibits goblet cell degranulation in a Guinea pig asthma model.
Allergol Int, 2012 Mar , 61 (133-42).

383

Brown KC et al. MG624, an α7-nAChR antagonist, inhibits angiogenesis via the Egr-1/FGF2 pathway.
Angiogenesis, 2012 Mar , 15 (99-114).

387

390

Miyazaki H et al. Differential regulation of a CLC anion channel by SPAK kinase ortholog-mediated multisite phosphorylation.
Am. J. Physiol., Cell Physiol., 2012 Jun , 302 (C1702-12).

391

Mao J et al. Cell cycle-dependent subcellular distribution of ClC-3 in HeLa cells.
Histochem. Cell Biol., 2012 Jun , 137 (763-76).

393

396

Feng L et al. Molecular mechanism of proton transport in CLC Cl-/H+ exchange transporters.
Proc. Natl. Acad. Sci. U.S.A., 2012 Jul 17 , 109 (11699-704).

398

399

400

Xue Y et al. Report of two Chinese patients suffering from CLCN7-related osteopetrosis and root dysplasia.
J Craniomaxillofac Surg, 2012 Jul , 40 (416-20).

401

Stauber T et al. Cell biology and physiology of CLC chloride channels and transporters.
Compr Physiol, 2012 Jul , 2 (1701-44).

403

Nighot PK et al. Chloride channel ClC-2 modulates tight junction barrier function via intracellular trafficking of occludin.
Am. J. Physiol., Cell Physiol., 2012 Jan , 302 (C178-87).

412

Cuddapah VA et al. Kinase activation of ClC-3 accelerates cytoplasmic condensation during mitotic cell rounding.
Am. J. Physiol., Cell Physiol., 2012 Feb , 302 (C527-38).

414

Tanikawa C et al. CLCA2 as a p53-inducible senescence mediator.
Neoplasia, 2012 Feb , 14 (141-9).

417

Lourdel S et al. ClC-5 mutations associated with Dent's disease: a major role of the dimer interface.
Pflugers Arch., 2012 Feb , 463 (247-56).

419

420

Wang LJ et al. [CLC-K chloride channel in the thick ascending limb of kidney and Bartter's syndrome].
Sheng Li Ke Xue Jin Zhan, 2012 Feb , 43 (51-4).

422

Alevy YG et al. IL-13-induced airway mucus production is attenuated by MAPK13 inhibition.
J. Clin. Invest., 2012 Dec 3 , 122 (4555-68).

423

Sasaki Y et al. CLCA2, a target of the p53 family, negatively regulates cancer cell migration and invasion.
Cancer Biol. Ther., 2012 Dec 1 , 13 (1512-21).

424

Lim HH et al. Intracellular proton access in a cl(-)/h(+) antiporter.
PLoS Biol., 2012 Dec , 10 (e1001441).

426

Wu WL et al. [Effects of dexamethasone on IL-13-induced mCLCA3 and Muc5ac expressions in nasal mucosa of rats].
Xi Bao Yu Fen Zi Mian Yi Xue Za Zhi, 2012 Dec , 28 (1258-60).

428

Chen ZT et al. [Analysis of CLCN1 gene mutations in 2 patients with myotonia congenita].
Zhonghua Yi Xue Yi Chuan Xue Za Zhi, 2012 Dec , 29 (690-2).

431

Gradogna A et al. Dissecting a regulatory calcium-binding site of CLC-K kidney chloride channels.
J. Gen. Physiol., 2012 Dec , 140 (681-96).

437

444

Lee BH et al. Genetic basis of Bartter syndrome in Korea.
Nephrol. Dial. Transplant., 2012 Apr , 27 (1516-21).

445

Coulibaly G et al. [Dent's syndrome. Nephrology follow-up of four patients of the same family].
Nephrol. Ther., 2012 Apr , 8 (92-5).

447

Hosseinzadeh Z et al. Downregulation of ClC-2 by JAK2.
Cell. Physiol. Biochem., 2012 , 29 (737-42).

449

Mindell JA Lysosomal acidification mechanisms.
Annu. Rev. Physiol., 2012 , 74 (69-86).

450

453

Bogusz A [The CIC chloride channels and their role in plant cell].
Postepy Biochem., 2012 , 58 (54-60).

457

Su X et al. Association of CLCNKB haplotypes and hypertension in Mongolian and Han populations.
Clin. Exp. Hypertens., 2012 , 34 (482-7).

459

461

Robitaille P et al. Bartter syndrome in two sisters with a novel mutation of the CLCNKB gene, one with deafness.
Eur. J. Pediatr., 2011 Sep , 170 (1209-11).

466

Ratté S et al. ClC-2 channels regulate neuronal excitability, not intracellular chloride levels.
J. Neurosci., 2011 Nov 2 , 31 (15838-43).

467

Zhang Y et al. The coupled proton transport in the ClC-ec1 Cl(-)/H(+) antiporter.
Biophys. J., 2011 Nov 16 , 101 (L47-9).

473

Majumdar A et al. Degradation of Alzheimer's amyloid fibrils by microglia requires delivery of ClC-7 to lysosomes.
Mol. Biol. Cell, 2011 May 15 , 22 (1664-76).

475

Claverie-Martín F et al. Dent's disease: clinical features and molecular basis.
Pediatr. Nephrol., 2011 May , 26 (693-704).

479

Deisz RA et al. Components of neuronal chloride transport in rat and human neocortex.
J. Physiol. (Lond.), 2011 Mar 15 , 589 (1317-47).

481

Lamb GD et al. On the localization of ClC-1 in skeletal muscle fibers.
J. Gen. Physiol., 2011 Mar , 137 (327-9; author reply 331-3).

488

Duan DD The ClC-3 chloride channels in cardiovascular disease.
Acta Pharmacol. Sin., 2011 Jun , 32 (675-84).

493

494

Shibata K et al. Effect of the release from mechanical stress on osteoclastogenesis in RAW264.7 cells.
Int. J. Mol. Med., 2011 Jul , 28 (73-9).

496

Matsunaga Y et al. Effects of a Janus kinase inhibitor, pyridone 6, on airway responses in a murine model of asthma.
Biochem. Biophys. Res. Commun., 2011 Jan 7 , 404 (261-7).

497

Kieseritzky G et al. Charge transport in the ClC-type chloride-proton anti-porter from Escherichia coli.
J. Biol. Chem., 2011 Jan 28 , 286 (2976-86).

499

Shuvaev VV et al. PECAM-targeted delivery of SOD inhibits endothelial inflammatory response.
FASEB J., 2011 Jan , 25 (348-57).

500

501

Cuthbert AW Lubiprostone targets prostanoid EP₄ receptors in ovine airways.
Br. J. Pharmacol., 2011 Jan , 162 (508-20).

504

Jayaram H et al. Structure of a slow CLC Cl⁻/H+ antiporter from a cyanobacterium.
Biochemistry, 2011 Feb 8 , 50 (788-94).

506

Al Ghouleh I et al. Endosomal ClC-3 and Nox1: moving marksmen of redox signaling?
Arterioscler. Thromb. Vasc. Biol., 2011 Feb , 31 (240-2).

508

Chu X et al. A critical role for chloride channel-3 (CIC-3) in smooth muscle cell activation and neointima formation.
Arterioscler. Thromb. Vasc. Biol., 2011 Feb , 31 (345-51).

510

511

Fallah G et al. TMEM16A(a)/anoctamin-1 shares a homodimeric architecture with CLC chloride channels.
Mol. Cell Proteomics, 2011 Feb , 10 (M110.004697).

513

Ye D et al. [ClC-3 siRNA inhibits regulatory volume decrease in nasopharyngeal carcinoma cells].
Nan Fang Yi Ke Da Xue Xue Bao, 2011 Feb , 31 (216-20).

515

De Stefano S et al. Extracellular determinants of anion discrimination of the Cl-/H+ antiporter protein CLC-5.
J. Biol. Chem., 2011 Dec 23 , 286 (44134-44).

517

Fong P Thyroid iodide efflux: a team effort?
J. Physiol. (Lond.), 2011 Dec 15 , 589 (5929-39).

518

Titulaer MJ et al. Lambert-Eaton myasthenic syndrome: from clinical characteristics to therapeutic strategies.
Lancet Neurol, 2011 Dec , 10 (1098-107).

521

525

He ML et al. Effects of ion channels on proliferation in cultured human cardiac fibroblasts.
J. Mol. Cell. Cardiol., 2011 Aug , 51 (198-206).

526

Nomura N et al. Generation and analyses of R8L barttin knockin mouse.
Am. J. Physiol. Renal Physiol., 2011 Aug , 301 (F297-307).

530

Ahnert-Hilger G et al. CLC-3 spices up GABAergic synaptic vesicles.
Nat. Neurosci., 2011 Apr , 14 (405-7).

531

Riazanski V et al. Presynaptic CLC-3 determines quantal size of inhibitory transmission in the hippocampus.
Nat. Neurosci., 2011 Apr , 14 (487-94).

532

Tseng PY et al. Binding of ATP to the CBS domains in the C-terminal region of CLC-1.
J. Gen. Physiol., 2011 Apr , 137 (357-68).

533

Grand T et al. Heterogeneity in the processing of CLCN5 mutants related to Dent disease.
Hum. Mutat., 2011 Apr , 32 (476-83).

535

Vieira AC et al. Ionic components of electric current at rat corneal wounds.
PLoS ONE, 2011 , 6 (e17411).

536

Jeck N et al. Loop disorders: insights derived from defined genotypes.
Nephron Physiol, 2011 , 118 (p7-14).

537

van Lunteren E et al. Fatigue-inducing stimulation resolves myotonia in a drug-induced model.
BMC Physiol., 2011 , 11 (5).

539

McCarthy J et al. Polystyrene nanoparticles activate ion transport in human airway epithelial cells.
Int J Nanomedicine, 2011 , 6 (1343-56).

542

Simske JS et al. Claudin family proteins in Caenorhabditis elegans.
Methods Mol. Biol., 2011 , 762 (147-69).

546

Jouret F et al. Segmental and subcellular distribution of CFTR in the kidney.
Methods Mol. Biol., 2011 , 741 (285-99).

548

Iqbal H et al. Identification of missense mutation (I12T) in the BSND gene and bioinformatics analysis.
J. Biomed. Biotechnol., 2011 , 2011 (304612).

550

Tang CY et al. Physiology and pathophysiology of CLC-1: mechanisms of a chloride channel disease, myotonia.
J. Biomed. Biotechnol., 2011 , 2011 (685328).

553

Vilasi A et al. Proteomics and tubulopathies.
J. Nephrol., 2010 Nov-Dec , 23 Suppl 16 (S221-7).

554

Lang F et al. SGK, renal function and hypertension.
J. Nephrol., 2010 Nov-Dec , 23 Suppl 16 (S124-9).

558

Wang H et al. Chloride channel ClC-3 promotion of osteogenic differentiation through Runx2.
J. Cell. Biochem., 2010 Sep 1 , 111 (49-58).

561

Földy C et al. Regulation of fast-spiking basket cell synapses by the chloride channel ClC-2.
Nat. Neurosci., 2010 Sep , 13 (1047-9).

562

Gradogna A et al. A regulatory calcium-binding site at the subunit interface of CLC-K kidney chloride channels.
J. Gen. Physiol., 2010 Sep , 136 (311-23).

564

Wang H et al. Osteogenic role of endosomal chloride channels in MC3T3-E1 cells.
Mol. Cell. Biochem., 2010 Sep , 342 (191-9).

566

Jentsch TJ et al. ClC-3--a granular anion transporter involved in insulin secretion?
Cell Metab., 2010 Oct 6 , 12 (307-8; author reply 309-10).

567

Giguère A et al. CLCA2, a novel RUNX1 partner gene in a therapy-related leukemia with t(1;21)(p22;q22).
Cancer Genet. Cytogenet., 2010 Oct 15 , 202 (94-100).

568

Matchkov VV Mechanisms of cellular synchronization in the vascular wall.
Dan Med Bull, 2010 Oct , 57 (B4191).

569

Stauber T et al. Sorting motifs of the endosomal/lysosomal CLC chloride transporters.
J. Biol. Chem., 2010 Nov 5 , 285 (34537-48).

570

573

574

Davis AJ et al. Expression profile and protein translation of TMEM16A in murine smooth muscle.
Am. J. Physiol., Cell Physiol., 2010 Nov , 299 (C948-59).

575

Bogdanović R et al. A novel CLCN5 mutation in a boy with Bartter-like syndrome and partial growth hormone deficiency.
Pediatr. Nephrol., 2010 Nov , 25 (2363-8).

577

581

Edwards JC et al. Chloride channels of intracellular membranes.
FEBS Lett., 2010 May 17 , 584 (2102-11).

582

Zifarelli G et al. CLC transport proteins in plants.
FEBS Lett., 2010 May 17 , 584 (2122-7).

584

Zifarelli G et al. The role of protons in fast and slow gating of the Torpedo chloride channel ClC-0.
Eur. Biophys. J., 2010 May , 39 (869-75).

586

Lyons MJ et al. Novel CLCN1 mutation in carbamazepine-responsive myotonia congenita.
Pediatr. Neurol., 2010 May , 42 (365-8).

592

Duran C et al. Chloride channels: often enigmatic, rarely predictable.
Annu. Rev. Physiol., 2010 Mar 17 , 72 (95-121).

593

Miloshevsky GV et al. Antiport mechanism for Cl(-)/H(+) in ClC-ec1 from normal-mode analysis.
Biophys. J., 2010 Mar 17 , 98 (999-1008).

596

Kumar KR et al. A novel CLCN1 mutation (G1652A) causing a mild phenotype of thomsen disease.
Muscle Nerve, 2010 Mar , 41 (412-5).

598

Braun J et al. Murine mCLCA5 is expressed in granular layer keratinocytes of stratified epithelia.
Histochem. Cell Biol., 2010 Mar , 133 (285-99).

599

Wood JD Enteric nervous system: sensory physiology, diarrhea and constipation.
Curr. Opin. Gastroenterol., 2010 Mar , 26 (102-8).

600

van der Doef HP et al. Association of the CLCA1 p.S357N variant with meconium ileus in European patients with cystic fibrosis.
J. Pediatr. Gastroenterol. Nutr., 2010 Mar , 50 (347-9).

601

Wu W et al. [Expression and clinical significance of calcium-activated chloride channel and mucins in nasal mucosa with allergic rhinitis].
Lin Chung Er Bi Yan Hou Tou Jing Wai Ke Za Zhi, 2010 Mar , 24 (193-5, 199).

605

Steinberg BE et al. A cation counterflux supports lysosomal acidification.
J. Cell Biol., 2010 Jun 28 , 189 (1171-86).

606

Smith AJ et al. Direct endosomal acidification by the outwardly rectifying CLC-5 Cl(-)/H(+) exchanger.
J. Physiol. (Lond.), 2010 Jun 15 , 588 (2033-45).

607

608

610

Cao L et al. Chloride channels and transporters in human corneal epithelium.
Exp. Eye Res., 2010 Jun , 90 (771-9).

611

Ding C et al. Duct system of the rabbit lacrimal gland: structural characteristics and role in lacrimal secretion.
Invest. Ophthalmol. Vis. Sci., 2010 Jun , 51 (2960-7).

616

Picollo A et al. Proton block of the CLC-5 Cl-/H+ exchanger.
J. Gen. Physiol., 2010 Jun , 135 (653-9).

617

von der Fecht-Bartenbach J et al. CLC-b-mediated NO-3/H+ exchange across the tonoplast of Arabidopsis vacuoles.
Plant Cell Physiol., 2010 Jun , 51 (960-8).

624

625

Sánchez-Rodríguez JE et al. Permeant anions contribute to voltage dependence of ClC-2 chloride channel by interacting with the protopore gate.
J. Physiol. (Lond.), 2010 Jul 15 , 588 (2545-56).

626

Braun NA et al. The yeast CLC protein counteracts vesicular acidification during iron starvation.
J. Cell. Sci., 2010 Jul 1 , 123 (2342-50).

627

628

Roussa E et al. Cellular distribution and subcellular localization of mCLCA1/2 in murine gastrointestinal epithelia.
J. Histochem. Cytochem., 2010 Jul , 58 (653-68).

629

Galanopoulou AS Mutations affecting GABAergic signaling in seizures and epilepsy.
Pflugers Arch., 2010 Jul , 460 (505-23).

631

Cederholm JM et al. Inter-subunit communication and fast gate integrity are important for common gating in hClC-1.
Int. J. Biochem. Cell Biol., 2010 Jul , 42 (1182-8).

632

Hauber HP et al. Effect of Th2 type cytokines on hCLCA1 and mucus expression in cystic fibrosis airways.
J. Cyst. Fibros., 2010 Jul , 9 (277-9).

634

Matsuda JJ et al. The ClC-3 Cl-/H+ antiporter becomes uncoupled at low extracellular pH.
J. Biol. Chem., 2010 Jan 22 , 285 (2569-79).

637

Niemeyer MI et al. No evidence for a role of CLCN2 variants in idiopathic generalized epilepsy.
Nat. Genet., 2010 Jan , 42 (3).

638

Wartosch L et al. A role for chloride transport in lysosomal protein degradation.
Autophagy, 2010 Jan , 6 (158-9).

641

Zhang S et al. Distinct roles of cholinergic receptors in small cell lung cancer cells.
Anticancer Res., 2010 Jan , 30 (97-106).

643

644

Zhang XD et al. Accessibility of the CLC-0 pore to charged methanethiosulfonate reagents.
Biophys. J., 2010 Feb 3 , 98 (377-85).

653

Tang YB et al. Volume-regulated chloride channels and cerebral vascular remodelling.
Clin. Exp. Pharmacol. Physiol., 2010 Feb , 37 (238-42).

654

Ko YJ et al. Chloride ion conduction without water coordination in the pore of ClC protein.
J Comput Chem, 2010 Feb , 31 (603-11).

655

Improgo MR et al. ASCL1 regulates the expression of the CHRNA5/A3/B4 lung cancer susceptibility locus.
Mol. Cancer Res., 2010 Feb , 8 (194-203).

657

658

Pressey SN et al. Distinct neuropathologic phenotypes after disrupting the chloride transport proteins ClC-6 or ClC-7/Ostm1.
J. Neuropathol. Exp. Neurol., 2010 Dec , 69 (1228-46).

660

662

Lueck JD et al. Sarcolemmal-restricted localization of functional ClC-1 channels in mouse skeletal muscle.
J. Gen. Physiol., 2010 Dec , 136 (597-613).

663

Tian M et al. Chloride channels regulate chondrogenesis in chicken mandibular mesenchymal cells.
Arch. Oral Biol., 2010 Dec , 55 (938-45).

664

Enríquez R et al. Gitelman syndrome due to p.A204T mutation in CLCNKB gene.
Int Urol Nephrol, 2010 Dec , 42 (1099-102).

668

Nighot PK et al. ClC-2 regulates mucosal barrier function associated with structural changes to the villus and epithelial tight junction.
Am. J. Physiol. Gastrointest. Liver Physiol., 2010 Aug , 299 (G449-56).

669

Lang F Modulation of ClC-K channel function by the accessory subunit barttin.
J. Am. Soc. Nephrol., 2010 Aug , 21 (1238-9).

670

Fischer M et al. Barttin activates ClC-K channel function by modulating gating.
J. Am. Soc. Nephrol., 2010 Aug , 21 (1281-9).

674

680

Suzuki S [Lambert-Eaton myasthenic syndrome (LEMS)]
Brain Nerve, 2010 Apr , 62 (419-26).

681

Phadke SR et al. Novel mutations in Indian patients with autosomal recessive infantile malignant osteopetrosis.
Indian J. Med. Res., 2010 Apr , 131 (508-14).

682

Scheper GC et al. Analysis of CLCN2 as candidate gene for megalencephalic leukoencephalopathy with subcortical cysts.
Genet Test Mol Biomarkers, 2010 Apr , 14 (255-7).

683

Hume JR et al. CLC-3 chloride channels in the pulmonary vasculature.
Adv. Exp. Med. Biol., 2010 , 661 (237-47).

687

De Lisle RC et al. Lubiprostone ameliorates the cystic fibrosis mouse intestinal phenotype.
BMC Gastroenterol, 2010 , 10 (107).

689

Devuyst O et al. Dent's disease.
Orphanet J Rare Dis, 2010 , 5 (28).

691

Carraro-Lacroix LR et al. Role of CFTR and ClC-5 in modulating vacuolar H+-ATPase activity in kidney proximal tubule.
Cell. Physiol. Biochem., 2010 , 26 (563-76).

692

Gradogna A et al. Molecular Pharmacology of Kidney and Inner Ear CLC-K Chloride Channels.
Front Pharmacol, 2010 , 1 (130).

695

Thompson CH et al. Isolation and characterization of a high affinity peptide inhibitor of ClC-2 chloride channels.
J. Biol. Chem., 2009 Sep 18 , 284 (26051-62).

697

Sethi SK et al. Vitamin A responsive night blindness in Dent's disease.
Pediatr. Nephrol., 2009 Sep , 24 (1765-70).

701

Kleefuss-Lie A et al. CLCN2 variants in idiopathic generalized epilepsy.
Nat. Genet., 2009 Sep , 41 (954-5).

702

703

Arzel-Hézode M et al. Homozygosity for dominant mutations increases severity of muscle channelopathies.
Muscle Nerve, 2009 Oct 30 , ().

704

Elvington SM et al. Substrate-driven conformational changes in ClC-ec1 observed by fluorine NMR.
EMBO J., 2009 Oct 21 , 28 (3090-102).

706

708

Zifarelli G et al. Intracellular regulation of human ClC-5 by adenine nucleotides.
EMBO Rep., 2009 Oct , 10 (1111-6).

710

Pedersen TH et al. Regulation of ClC-1 and KATP channels in action potential-firing fast-twitch muscle fibers.
J. Gen. Physiol., 2009 Oct , 134 (309-22).

713

Deriy LV et al. The granular chloride channel ClC-3 is permissive for insulin secretion.
Cell Metab., 2009 Oct , 10 (316-23).

715

Lang F et al. Targeting SGK1 in diabetes.
Expert Opin. Ther. Targets, 2009 Nov , 13 (1303-11).

717

Johnson M et al. Characteristics of Cl- uptake in rat alveolar type I cells.
Am. J. Physiol. Lung Cell Mol. Physiol., 2009 Nov , 297 (L816-27).

718

Ravva P et al. Population pharmacokinetic analysis of varenicline in adult smokers.
Br J Clin Pharmacol, 2009 Nov , 68 (669-81).

720

Hamann M et al. Human ClCa1 modulates anionic conduction of calcium-dependent chloride currents.
J. Physiol. (Lond.), 2009 May 15 , 587 (2255-74).

721

722

Plans V et al. Physiological roles of CLC Cl(-)/H (+) exchangers in renal proximal tubules.
Pflugers Arch., 2009 May , 458 (23-37).

723

Jung J et al. Allelic-based gene-gene interaction associated with quantitative traits.
Genet. Epidemiol., 2009 May , 33 (332-43).

724

Brochard K et al. Phenotype-genotype correlation in antenatal and neonatal variants of Bartter syndrome.
Nephrol. Dial. Transplant., 2009 May , 24 (1455-64).

725

Joo NS et al. Lubiprostone stimulates secretion from tracheal submucosal glands of sheep, pigs, and humans.
Am. J. Physiol. Lung Cell Mol. Physiol., 2009 May , 296 (L811-24).

727

Alekov AK et al. Channel-like slippage modes in the human anion/proton exchanger ClC-4.
J. Gen. Physiol., 2009 May , 133 (485-96).

728

Haggie PM et al. Unimpaired lysosomal acidification in respiratory epithelial cells in cystic fibrosis.
J. Biol. Chem., 2009 Mar 20 , 284 (7681-6).

730

Lew RR et al. Transient responses during hyperosmotic shock in the filamentous fungus Neurospora crassa.
Microbiology (Reading, Engl.), 2009 Mar , 155 (903-11).

731

Planells-Cases R et al. Chloride channelopathies.
Biochim. Biophys. Acta, 2009 Mar , 1792 (173-89).

732

Wu WL et al. [Effects of glucocorticoid on calcium-activated chloride channel expression in nasal mucosa in allergic rhinitis rats].
Zhonghua Er Bi Yan Hou Tou Jing Wai Ke Za Zhi, 2009 Mar , 44 (242-5).

734

Paleari L et al. Inhibition of nonneuronal alpha7-nicotinic receptor for lung cancer treatment.
Am. J. Respir. Crit. Care Med., 2009 Jun 15 , 179 (1141-50).

735

Ma L et al. Functional study of cytoplasmic loops of human skeletal muscle chloride channel, hClC-1.
Int. J. Biochem. Cell Biol., 2009 Jun , 41 (1402-9).

736

Trip J et al. Redefining the clinical phenotypes of non-dystrophic myotonic syndromes.
J. Neurol. Neurosurg. Psychiatr., 2009 Jun , 80 (647-52).

738

Winpenny JP et al. The CLCA gene family: putative therapeutic target for respiratory diseases.
Inflamm Allergy Drug Targets, 2009 Jun , 8 (146-60).

742

Zhao Q et al. CLC-7: a potential therapeutic target for the treatment of osteoporosis and neurodegeneration.
Biochem. Biophys. Res. Commun., 2009 Jul 3 , 384 (277-9).

743

745

747

Krueger D et al. The multi-herbal drug STW 5 (Iberogast(R)) has prosecretory action in the human intestine.
Neurogastroenterol. Motil., 2009 Jan 30 , ().

748

De Angeli A et al. Review. CLC-mediated anion transport in plant cells.
Philos. Trans. R. Soc. Lond., B, Biol. Sci., 2009 Jan 27 , 364 (195-201).

749

Lísal J et al. Review. Proton-coupled gating in chloride channels.
Philos. Trans. R. Soc. Lond., B, Biol. Sci., 2009 Jan 27 , 364 (181-7).

750

Miller C et al. A provisional transport mechanism for a chloride channel-type Cl-/H+ exchanger.
Philos. Trans. R. Soc. Lond., B, Biol. Sci., 2009 Jan 27 , 364 (175-80).

751

Henriksen K et al. Characterization of acid flux in osteoclasts from patients harboring a G215R mutation in ClC-7.
Biochem. Biophys. Res. Commun., 2009 Jan 23 , 378 (804-9).

756

Janssen AG et al. Disease-causing dysfunctions of barttin in Bartter syndrome type IV.
J. Am. Soc. Nephrol., 2009 Jan , 20 (145-53).

757

758

Zhang XD et al. Blocking pore-open mutants of CLC-0 by amphiphilic blockers.
J. Gen. Physiol., 2009 Jan , 133 (43-58).

759

Zhang XD et al. Amphiphilic blockers punch through a mutant CLC-0 pore.
J. Gen. Physiol., 2009 Jan , 133 (59-68).

762

Planells-Cases R et al. Chloride channelopathies.
Biochim. Biophys. Acta, 2009 Feb 9 , ().

764

Hohberger B et al. Cereblon is expressed in the retina and binds to voltage-gated chloride channels.
FEBS Lett., 2009 Feb 18 , 583 (633-7).

768

Lim HH et al. Intracellular proton-transfer mutants in a CLC Cl-/H+ exchanger.
J. Gen. Physiol., 2009 Feb , 133 (131-8).

770

Sile S et al. CLCNKB-T481S and essential hypertension in a Ghanaian population.
J. Hypertens., 2009 Feb , 27 (298-304).

771

Carraro-Lacroix LR et al. Physiological implications of the regulation of vacuolar H+-ATPase by chloride ions.
Braz. J. Med. Biol. Res., 2009 Feb , 42 (155-63).

772

773

Stechman MJ et al. Genetic causes of hypercalciuric nephrolithiasis.
Pediatr. Nephrol., 2009 Dec , 24 (2321-32).

777

Frishberg Y et al. Dent's disease manifesting as focal glomerulosclerosis: Is it the tip of the iceberg?
Pediatr. Nephrol., 2009 Dec , 24 (2369-73).

778

779

Moon IS et al. Novel CLCN1 mutations and clinical features of Korean patients with myotonia congenita.
J. Korean Med. Sci., 2009 Dec , 24 (1038-44).

780

Duan X et al. ClC-5 regulates dentin development through TGF-beta1 pathway.
Arch. Oral Biol., 2009 Dec , 54 (1118-24).

781

Besbas N et al. A novel CLCN7 mutation resulting in a most severe form of autosomal recessive osteopetrosis.
Eur. J. Pediatr., 2009 Dec , 168 (1449-54).

782

Walia V et al. hCLCA2 Is a p53-Inducible Inhibitor of Breast Cancer Cell Proliferation.
Cancer Res., 2009 Aug 15 , 69 (6624-32).

787

Mazzolari E et al. A single-center experience in 20 patients with infantile malignant osteopetrosis.
Am. J. Hematol., 2009 Aug , 84 (473-9).

789

Bergsdorf EY et al. Residues important for nitrate/proton coupling in plant and mammalian CLC transporters.
J. Biol. Chem., 2009 Apr 24 , 284 (11184-93).

790

Osborne RJ et al. Transcriptional and post-transcriptional impact of toxic RNA in myotonic dystrophy.
Hum. Mol. Genet., 2009 Apr 15 , 18 (1471-81).

792

Klaus F et al. PIKfyve-dependent regulation of the Cl- channel ClC-2.
Biochem. Biophys. Res. Commun., 2009 Apr 10 , 381 (407-11).

793

Pusch M et al. It's the proton also in ClC-2.
J. Physiol. (Lond.), 2009 Apr 1 , 587 (1379-80).

795

Jouret F et al. CFTR and defective endocytosis: new insights in the renal phenotype of cystic fibrosis.
Pflugers Arch., 2009 Apr , 457 (1227-36).

796

Xiong D et al. Cardiac-specific overexpression of the human short CLC-3 chloride channel isoform in mice.
Clin. Exp. Pharmacol. Physiol., 2009 Apr , 36 (386-93).

797

798

799

Zdebik AA Statins and fibrate target ClC-1 - from side effects to CLC pharmacology.
Br. J. Pharmacol., 2009 Apr , 156 (1204-5).

801

Ward JM et al. Plant ion channels: gene families, physiology, and functional genomics analyses.
Annu. Rev. Physiol., 2009 , 71 (59-82).

802

Patel AC et al. The role of CLCA proteins in inflammatory airway disease.
Annu. Rev. Physiol., 2009 , 71 (425-49).

806

Shrimpton AE et al. OCRL1 mutations in Dent 2 patients suggest a mechanism for phenotypic variability.
Nephron Physiol, 2009 , 112 (p27-36).

809

810

Izuhara K et al. The mechanism of mucus production in bronchial asthma.
Curr. Med. Chem., 2009 , 16 (2867-75).

813

Braun AP Identification of ClC-7 as a major pathway for Cl- movement in lysosomes.
Channels (Austin), 2008 Sep-Oct , 2 (309).

814

Braun AP All in the family: ClC transporters and channels may share common ancestry.
Channels (Austin), 2008 Sep-Oct , 2 (308).

815

Mankodi A Myotonic disorders.
, 2008 Jul-Sep , 56 (298-304).

816

Jentsch TJ CLC chloride channels and transporters: from genes to protein structure, pathology and physiology.
Crit. Rev. Biochem. Mol. Biol., 2008 Jan-Feb , 43 (3-36).

818

Maddison P et al. Paraneoplastic neurological autoimmunity and survival in small-cell lung cancer.
J. Neuroimmunol., 2008 Sep 15 , 201-202 (159-62).

819

Habela CW et al. ClC3 is a critical regulator of the cell cycle in normal and malignant glial cells.
J. Neurosci., 2008 Sep 10 , 28 (9205-17).

820

Hou J et al. ClC chloride channels in tooth germ and odontoblast-like MDPC-23 cells.
Arch. Oral Biol., 2008 Sep , 53 (874-8).

822

Henriksen K et al. Ion transporters involved in acidification of the resorption lacuna in osteoclasts.
Calcif. Tissue Int., 2008 Sep , 83 (230-42).

823

824

Maritzen T et al. Role of the vesicular chloride transporter ClC-3 in neuroendocrine tissue.
J. Neurosci., 2008 Oct 15 , 28 (10587-98).

828

Zhang XD et al. ATP inhibition of CLC-1 is controlled by oxidation and reduction.
J. Gen. Physiol., 2008 Oct , 132 (421-8).

831

Alekov AK et al. Anion channels: regulation of ClC-3 by an orphan second messenger.
Curr. Biol., 2008 Nov 25 , 18 (R1061-4).

832

Huber SM et al. Organic osmolyte channels in malaria-infected erythrocytes.
Biochem. Biophys. Res. Commun., 2008 Nov 21 , 376 (514-8).

833

Osteen JD et al. Insights into the ClC-4 transport mechanism from studies of Zn2+ inhibition.
Biophys. J., 2008 Nov 15 , 95 (4668-75).

835

Arreola J et al. Gating and trafficking of ClC-2 chloride channel without cystathionine beta-synthase domains.
J. Physiol. (Lond.), 2008 Nov 15 , 586 (5289).

836

Garcia-Olivares J et al. Gating of human ClC-2 chloride channels and regulation by carboxy-terminal domains.
J. Physiol. (Lond.), 2008 Nov 15 , 586 (5325-36).

837

Nijenhuis T et al. Bone resorption inhibitor alendronate normalizes the reduced bone thickness of TRPV5(-/-) mice.
J. Bone Miner. Res., 2008 Nov , 23 (1815-24).

840

Romanenko VG et al. Clcn2 encodes the hyperpolarization-activated chloride channel in the ducts of mouse salivary glands.
Am. J. Physiol. Gastrointest. Liver Physiol., 2008 Nov , 295 (G1058-67).

841

MacDonald KD et al. Lubiprostone activates non-CFTR-dependent respiratory epithelial chloride secretion in cystic fibrosis mice.
Am. J. Physiol. Lung Cell Mol. Physiol., 2008 Nov , 295 (L933-40).

845

Thomas J et al. Recessive CLCN1 mutation presenting as Thomsen disease.
Muscle Nerve, 2008 Nov , 38 (1515-7).

848

Wright J et al. Transcriptional adaptation to Clcn5 knockout in proximal tubules of mouse kidney.
Physiol. Genomics, 2008 May 13 , 33 (341-54).

849

Mao J et al. Suppression of ClC-3 channel expression reduces migration of nasopharyngeal carcinoma cells.
Biochem. Pharmacol., 2008 May 1 , 75 (1706-16).

851

Bassil AK et al. Activation of prostaglandin EP receptors by lubiprostone in rat and human stomach and colon.
Br. J. Pharmacol., 2008 May , 154 (126-35).

853

855

Sabater L et al. SOX1 antibodies are markers of paraneoplastic Lambert-Eaton myasthenic syndrome.
Neurology, 2008 Mar 18 , 70 (924-8).

861

Feng Q et al. DNA methylation in tumor and matched normal tissues from non-small cell lung cancer patients.
Cancer Epidemiol. Biomarkers Prev., 2008 Mar , 17 (645-54).

862

Sheffer-Babila S et al. Growth hormone improves growth rate and preserves renal function in Dent disease.
J. Pediatr. Endocrinol. Metab., 2008 Mar , 21 (279-86).

864

865

Martin-Moutot N et al. Distinct evolution of calcium channel antibody types in Lambert-Eaton myasthenic syndrome.
J. Neuroimmunol., 2008 Jun 15 , 197 (47-53).

867